| E803 | Defects of catalase and peroxidase |
| E804 | Gilbert syndrome |
| E805 | Crigler-Najjar syndrome |
| E806 | Other disorders of bilirubin metabolism |
| E807 | Disorder of bilirubin metabolism, unspecified |
| E83 | Disorders of mineral metabolism |
| E830 | Disorders of copper metabolism |
| E8300 | Disorder of copper metabolism, unspecified |
| E8301 | Wilson's disease |
| E8309 | Other disorders of copper metabolism |
| E831 | Disorders of iron metabolism |
| E8310 | Disorder of iron metabolism, unspecified |
| E8311 | Hemochromatosis |
| E83110 | Hereditary hemochromatosis |
| E83111 | Hemochromatosis due to repeated red blood cell transfusions |
| E83118 | Other hemochromatosis |
| E83119 | Hemochromatosis, unspecified |
| E8319 | Other disorders of iron metabolism |
| E832 | Disorders of zinc metabolism |
| E833 | Disorders of phosphorus metabolism and phosphatases |
| E8330 | Disorder of phosphorus metabolism, unspecified |
| E8331 | Familial hypophosphatemia |
| E8332 | Hereditary vitamin D-dependent rickets (type 1) (type 2) |
| E8339 | Other disorders of phosphorus metabolism |
| E834 | Disorders of magnesium metabolism |
| E8340 | Disorders of magnesium metabolism, unspecified |
| E8341 | Hypermagnesemia |
| E8342 | Hypomagnesemia |
| E8349 | Other disorders of magnesium metabolism |
| E835 | Disorders of calcium metabolism |
| E8350 | Unspecified disorder of calcium metabolism |
| E8351 | Hypocalcemia |
| E8352 | Hypercalcemia |
| E8359 | Other disorders of calcium metabolism |
| E838 | Other disorders of mineral metabolism |
| E8381 | Hungry bone syndrome |
| E8389 | Other disorders of mineral metabolism |
| E839 | Disorder of mineral metabolism, unspecified |
| E84 | Cystic fibrosis |
| E840 | Cystic fibrosis with pulmonary manifestations |
| E841 | Cystic fibrosis with intestinal manifestations |
| E8411 | Meconium ileus in cystic fibrosis |
| E8419 | Cystic fibrosis with other intestinal manifestations |
| E848 | Cystic fibrosis with other manifestations |
| E849 | Cystic fibrosis, unspecified |
| E85 | Amyloidosis |
| E850 | Non-neuropathic heredofamilial amyloidosis |
| E851 | Neuropathic heredofamilial amyloidosis |
| E852 | Heredofamilial amyloidosis, unspecified |
| E853 | Secondary systemic amyloidosis |