ICD-10-CM codes

97,584 codes · page 100 of 1,952

ICD-10Description
E76210 Morquio A mucopolysaccharidoses
E76211 Morquio B mucopolysaccharidoses
E76219 Morquio mucopolysaccharidoses, unspecified
E7622 Sanfilippo mucopolysaccharidoses
E7629 Other mucopolysaccharidoses
E763 Mucopolysaccharidosis, unspecified
E768 Other disorders of glucosaminoglycan metabolism
E769 Glucosaminoglycan metabolism disorder, unspecified
E77 Disorders of glycoprotein metabolism
E770 Defects in post-translational modification of lysosomal enzymes
E771 Defects in glycoprotein degradation
E778 Other disorders of glycoprotein metabolism
E779 Disorder of glycoprotein metabolism, unspecified
E78 Disorders of lipoprotein metabolism and other lipidemias
E780 Pure hypercholesterolemia
E7800 Pure hypercholesterolemia, unspecified
E7801 Familial hypercholesterolemia
E781 Pure hyperglyceridemia
E782 Mixed hyperlipidemia
E783 Hyperchylomicronemia
E784 Other hyperlipidemia
E7841 Elevated Lipoprotein(a)
E7849 Other hyperlipidemia
E785 Hyperlipidemia, unspecified
E786 Lipoprotein deficiency
E787 Disorders of bile acid and cholesterol metabolism
E7870 Disorder of bile acid and cholesterol metabolism, unspecified
E7871 Barth syndrome
E7872 Smith-Lemli-Opitz syndrome
E7879 Other disorders of bile acid and cholesterol metabolism
E788 Other disorders of lipoprotein metabolism
E7881 Lipoid dermatoarthritis
E7889 Other lipoprotein metabolism disorders
E789 Disorder of lipoprotein metabolism, unspecified
E79 Disorders of purine and pyrimidine metabolism
E790 Hyperuricemia w/o signs of inflam arthrit and tophaceous dis Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
E791 Lesch-Nyhan syndrome
E792 Myoadenylate deaminase deficiency
E798 Other disorders of purine and pyrimidine metabolism
E7981 Aicardi-Goutieres syndrome
E7982 Hereditary xanthinuria
E7989 Other specified disorders of purine and pyrimidine metabolism
E799 Disorder of purine and pyrimidine metabolism, unspecified
E80 Disorders of porphyrin and bilirubin metabolism
E800 Hereditary erythropoietic porphyria
E801 Porphyria cutanea tarda
E802 Other and unspecified porphyria
E8020 Unspecified porphyria
E8021 Acute intermittent (hepatic) porphyria
E8029 Other porphyria

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