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ICD-10-CM codes
97,584 codes · page 100 of 1,952
ICD-10
Description
E76210
Morquio A mucopolysaccharidoses
E76211
Morquio B mucopolysaccharidoses
E76219
Morquio mucopolysaccharidoses, unspecified
E7622
Sanfilippo mucopolysaccharidoses
E7629
Other mucopolysaccharidoses
E763
Mucopolysaccharidosis, unspecified
E768
Other disorders of glucosaminoglycan metabolism
E769
Glucosaminoglycan metabolism disorder, unspecified
E77
Disorders of glycoprotein metabolism
E770
Defects in post-translational modification of lysosomal enzymes
E771
Defects in glycoprotein degradation
E778
Other disorders of glycoprotein metabolism
E779
Disorder of glycoprotein metabolism, unspecified
E78
Disorders of lipoprotein metabolism and other lipidemias
E780
Pure hypercholesterolemia
E7800
Pure hypercholesterolemia, unspecified
E7801
Familial hypercholesterolemia
E781
Pure hyperglyceridemia
E782
Mixed hyperlipidemia
E783
Hyperchylomicronemia
E784
Other hyperlipidemia
E7841
Elevated Lipoprotein(a)
E7849
Other hyperlipidemia
E785
Hyperlipidemia, unspecified
E786
Lipoprotein deficiency
E787
Disorders of bile acid and cholesterol metabolism
E7870
Disorder of bile acid and cholesterol metabolism, unspecified
E7871
Barth syndrome
E7872
Smith-Lemli-Opitz syndrome
E7879
Other disorders of bile acid and cholesterol metabolism
E788
Other disorders of lipoprotein metabolism
E7881
Lipoid dermatoarthritis
E7889
Other lipoprotein metabolism disorders
E789
Disorder of lipoprotein metabolism, unspecified
E79
Disorders of purine and pyrimidine metabolism
E790
Hyperuricemia w/o signs of inflam arthrit and tophaceous dis Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
E791
Lesch-Nyhan syndrome
E792
Myoadenylate deaminase deficiency
E798
Other disorders of purine and pyrimidine metabolism
E7981
Aicardi-Goutieres syndrome
E7982
Hereditary xanthinuria
E7989
Other specified disorders of purine and pyrimidine metabolism
E799
Disorder of purine and pyrimidine metabolism, unspecified
E80
Disorders of porphyrin and bilirubin metabolism
E800
Hereditary erythropoietic porphyria
E801
Porphyria cutanea tarda
E802
Other and unspecified porphyria
E8020
Unspecified porphyria
E8021
Acute intermittent (hepatic) porphyria
E8029
Other porphyria
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