| 101824-1 | Aspartylglucosaminidase |
| 14168-9 | Palatinase (Tissue) |
| 14178-8 | Sucrase (Tissue) |
| 16574-6 | Cerebroside sulfatase (Tissue) |
| 16578-7 | Cerebroside sulfatase B (Tissue) |
| 1699-8 | Alpha-L-iduronidase (Tissue) |
| 1812-7 | Alpha fucosidase (Tissue) |
| 1815-0 | Acid alpha glucosidase (Tissue) |
| 1819-2 | Alpha mannosidase (Tissue) |
| 18366-5 | Cytochrome C oxidase (Tissue) |
| 1838-2 | Alpha-N-acetylglucosaminidase (Tissue) |
| 1899-4 | Argininosuccinate synthase (Tissue) |
| 1942-2 | Beta galactosidase (Tissue) |
| 1944-8 | Beta glucuronidase (Tissue) |
| 1955-4 | Beta-N-acetylhexosaminidase (Tissue) |
| 2017-2 | Carbamoyl phosphate synthetase (ammonia) (Tissue) |
| 2060-2 | Cerebroside sulfatase (Tissue) |
| 20758-9 | Cholinesterase in Brain |
| 2210-3 | Dihydrolipoamide acetyl transferase (Tissue) |
| 2211-1 | Dihydrolipoamide dehydrogenase (Tissue) |
| 2315-0 | Galactosylceramidase (Tissue) |
| 2316-8 | Galactosylgalactosylglucosylceramidase (Tissue) |
| 2355-6 | Glucose-6-Phosphatase (Tissue) |
| 2361-4 | Glucosylceramidase (Tissue) |
| 2375-4 | Glutaryl CoA dehydrogenase (Tissue) |
| 24043-2 | Acetyl-CoA:glucosamine acetyltransferase in Fibroblast |
| 24044-0 | Acetyl-CoA:glucosamine acetyltransferase in Leukocytes |
| 24046-5 | Alpha fucosidase in Fibroblast |
| 24047-3 | Alpha fucosidase in Leukocytes |
| 24048-1 | Alpha galactosidase A in Fibroblast |
| 24049-9 | Alpha galactosidase A in Leukocytes |
| 24050-7 | Acid alpha glucosidase in Fibroblast |
| 24051-5 | Acid alpha glucosidase in Leukocytes |
| 24052-3 | Alpha mannosidase in Fibroblast |
| 24053-1 | Alpha mannosidase in Leukocytes |
| 24054-9 | Alpha-N-acetylgalactosaminidase in Fibroblast |
| 24055-6 | Alpha-N-acetylgalactosaminidase in Leukocytes |
| 24056-4 | Alpha-L-iduronidase in Fibroblast |
| 24057-2 | Alpha-L-iduronidase in Leukocytes |
| 24058-0 | Aspartylglucosaminidase in Fibroblast |
| 24059-8 | Aspartylglucosaminidase in Leukocytes |
| 24060-6 | Beta galactosidase in Fibroblast |
| 24061-4 | Beta galactosidase in Leukocytes |
| 24064-8 | Beta glucuronidase in Fibroblast |
| 24065-5 | Beta glucuronidase in Leukocytes |
| 24067-1 | Beta mannosidase in Fibroblast |
| 24068-9 | Beta mannosidase in Leukocytes |
| 24072-1 | Beta-N-acetylhexosaminidase.B in Fibroblast |
| 24073-9 | Beta-N-acetylhexosaminidase.B in Leukocytes |
| 24074-7 | Beta-N-acetylhexosaminidase in Fibroblast |
| 24075-4 | Beta-N-acetylhexosaminidase in Leukocytes |
| 24077-0 | Cerebroside sulfatase in Fibroblast |
| 24078-8 | Cerebroside sulfatase in Leukocytes |
| 24079-6 | Cholesterol esterase in Fibroblast |
| 24080-4 | Cholesterol esterase in Leukocytes |
| 24081-2 | Dihydroxyacetone phosphate acylcoa acyl transferase in Fibroblast |
| 24082-0 | Galactose 1 phosphate uridyl transferase (Red Blood Cells) |
| 24083-8 | Galactosylceramidase in Fibroblast |
| 24084-6 | Galactosylceramidase in Leukocytes |
| 24085-3 | Heparan-N-sulfatase in Fibroblast |
| 24086-1 | Heparan-N-sulfatase in Leukocytes |
| 24088-7 | Iduronate-2-Sulfatase in Fibroblast |
| 24089-5 | Iduronate-2-Sulfatase in Leukocytes |
| 24091-1 | Alpha-N-acetylglucosaminidase in Fibroblast |
| 24092-9 | Alpha-N-acetylglucosaminidase in Leukocytes |
| 24093-7 | N-Acetylgalactosamine-4-Sulfatase in Fibroblast |
| 24094-5 | N-Acetylgalactosamine-4-Sulfatase in Leukocytes |
| 24095-2 | N-Acetylgalactosamine-6-Sulfatase in Fibroblast |
| 24096-0 | N-Acetylgalactosamine-6-Sulfatase in Leukocytes |
| 24097-8 | N-Acetylglucosamine-6-Sulfatase in Fibroblast |
| 24098-6 | N-Acetylglucosamine-6-Sulfatase in Leukocytes |
| 24099-4 | Sialidase in Fibroblast |
| 24100-0 | Acid sphingomyelinase in Fibroblast |
| 24101-8 | Acid sphingomyelinase in Leukocytes |
| 2455-4 | Hypoxanthine phosphoribosyltransferase (Tissue) |
| 2456-2 | Iduronate-2-Sulfatase (Tissue) |
| 25375-7 | Chymotrypsin (Stool) |
| 25829-3 | Glucosylceramidase in Fibroblast |
| 25831-9 | Beta-N-acetylhexosaminidase.A in Fibroblast |
| 2647-6 | N-Acetylgalactosamine-4-Sulfatase (Tissue) |
| 2649-2 | N-Acetylgalactosamine-6-Sulfatase (Tissue) |
| 2848-0 | Proline dipeptidase (Tissue) |
| 2850-6 | Propionyl CoA Carboxylase (Tissue) |
| 2899-3 | Purine nucleoside phosphorylase (Tissue) |
| 2909-0 | Pyruvate carboxylase (Tissue) |
| 2911-6 | Pyruvate dehydrogenase.lipoamide (Tissue) |
| 2946-2 | Sialidase (Tissue) |
| 29542-8 | Beta-N-acetylhexosaminidase cells (Amniotic Fluid) |
| 29639-2 | Alkaline phosphatase (Tissue) |
| 29640-0 | Isomaltase (Tissue) |
| 30315-6 | Acid alpha glucosidase in Small intestine Tissue |
| 30319-8 | Beta galactosidase in Small intestine Tissue |
| 30372-7 | Sucrase in Small intestine Tissue |
| 3101-3 | Uridyl transferase (Tissue) |
| 32233-9 | Carbamoyl phosphate synthetase (Tissue) |
| 32540-7 | Glucosylceramidase in Leukocytes |
| 32546-4 | Glucose-6-Phosphate dehydrogenase (Red Blood Cells) |
| 32552-2 | Pyruvate kinase (Red Blood Cells) |
| 32617-3 | Ornithine carbamoyltransferase (Tissue) |
| 32627-2 | Argininosuccinate lyase (Red Blood Cells) |