| 13741-4 | Ethylmalonate/Creat Ur | required |
| 13777-8 | Me-succinate/Creat Ur | required |
| 13748-9 | Glutarate/Creat Ur | required |
| 38360-4 | Isobutyrylgly/Creat Ur | required |
| 27892-9 | Butyrylgly/Creat Ur | required |
| 27097-5 | 2Me-butyrylglycine/Creat Ur | required |
| 13766-1 | Isovalerylgly/Creat Ur | required |
| 13753-9 | Hexanoylgly/Creat Ur | required |
| 99059-8 | N-acetylglycine/Creat Ur | |
| 38367-9 | n-octanoylgly/Creat Ur | required |
| 13793-5 | PPG/Creat Ur | required |
| 13811-5 | Suberylgly/Creat Ur | required |
| 38417-2 | tr-Cinnamoylgly/Creat Ur | required |
| 13732-3 | DDDA/Creat Ur | required |
| 50333-4 | Tdecanedioate/Creat Ur | required |
| 50332-6 | Hexadecanedioate/Creat Ur | required |
| 53718-3 | Acylglycines Ur-Imp | optional |
| 50334-2 | Acylglycines Pnl Ur | |