| D815 | Purine nucleoside phosphorylase [PNP] deficiency |
| D816 | Major histocompatibility complex class I deficiency |
| D817 | Major histocompatibility complex class II deficiency |
| D818 | Other combined immunodeficiencies |
| D8181 | Biotin-dependent carboxylase deficiency |
| D81810 | Biotinidase deficiency |
| D81818 | Other biotin-dependent carboxylase deficiency |
| D81819 | Biotin-dependent carboxylase deficiency, unspecified |
| D8182 | Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
| D8189 | Other combined immunodeficiencies |
| D819 | Combined immunodeficiency, unspecified |
| D82 | Immunodeficiency associated with other major defects |
| D820 | Wiskott-Aldrich syndrome |
| D821 | Di George's syndrome |
| D822 | Immunodeficiency with short-limbed stature |
| D823 | Immunodeficiency following hereditary defective response to Epstein-Barr virus |
| D824 | Hyperimmunoglobulin E [IgE] syndrome |
| D828 | Immunodeficiency associated with other specified major defects |
| D829 | Immunodeficiency associated with major defect, unspecified |
| D83 | Common variable immunodeficiency |
| D830 | Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function |
| D831 | Common variable immunodeficiency with predominant immunoregulatory T-cell disorders |
| D832 | Common variable immunodeficiency with autoantibodies to B- or T-cells |
| D838 | Other common variable immunodeficiencies |
| D839 | Common variable immunodeficiency, unspecified |
| D84 | Other immunodeficiencies |
| D840 | Lymphocyte function antigen-1 [LFA-1] defect |
| D841 | Defects in the complement system |
| D848 | Other specified immunodeficiencies |
| D8481 | Immunodeficiency due to conditions classified elsewhere |
| D8482 | Immunodeficiency due to drugs and external causes |
| D84821 | Immunodeficiency due to drugs |
| D84822 | Immunodeficiency due to external causes |
| D8489 | Other immunodeficiencies |
| D849 | Immunodeficiency, unspecified |
| D86 | Sarcoidosis |
| D860 | Sarcoidosis of lung |
| D861 | Sarcoidosis of lymph nodes |
| D862 | Sarcoidosis of lung with sarcoidosis of lymph nodes |
| D863 | Sarcoidosis of skin |
| D868 | Sarcoidosis of other sites |
| D8681 | Sarcoid meningitis |
| D8682 | Multiple cranial nerve palsies in sarcoidosis |
| D8683 | Sarcoid iridocyclitis |
| D8684 | Sarcoid pyelonephritis |
| D8685 | Sarcoid myocarditis |
| D8686 | Sarcoid arthropathy |
| D8687 | Sarcoid myositis |
| D8689 | Sarcoidosis of other sites |
| D869 | Sarcoidosis, unspecified |