| D531 | Other megaloblastic anemias, not elsewhere classified |
| D532 | Scorbutic anemia |
| D538 | Other specified nutritional anemias |
| D539 | Nutritional anemia, unspecified |
| D55 | Anemia due to enzyme disorders |
| D550 | Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency |
| D551 | Anemia due to other disorders of glutathione metabolism |
| D552 | Anemia due to disorders of glycolytic enzymes |
| D5521 | Anemia due to pyruvate kinase deficiency |
| D5529 | Anemia due to other disorders of glycolytic enzymes |
| D553 | Anemia due to disorders of nucleotide metabolism |
| D558 | Other anemias due to enzyme disorders |
| D559 | Anemia due to enzyme disorder, unspecified |
| D56 | Thalassemia |
| D560 | Alpha thalassemia |
| D561 | Beta thalassemia |
| D562 | Delta-beta thalassemia |
| D563 | Thalassemia minor |
| D564 | Hereditary persistence of fetal hemoglobin [HPFH] |
| D565 | Hemoglobin E-beta thalassemia |
| D568 | Other thalassemias |
| D569 | Thalassemia, unspecified |
| D57 | Sickle-cell disorders |
| D570 | Hb-SS disease with crisis |
| D5700 | Hb-SS disease with crisis, unspecified |
| D5701 | Hb-SS disease with acute chest syndrome |
| D5702 | Hb-SS disease with splenic sequestration |
| D5703 | Hb-SS disease with cerebral vascular involvement |
| D5704 | Hb-SS disease with dactylitis |
| D5709 | Hb-SS disease with crisis with other specified complication |
| D571 | Sickle-cell disease without crisis |
| D572 | Sickle-cell/Hb-C disease |
| D5720 | Sickle-cell/Hb-C disease without crisis |
| D5721 | Sickle-cell/Hb-C disease with crisis |
| D57211 | Sickle-cell/Hb-C disease with acute chest syndrome |
| D57212 | Sickle-cell/Hb-C disease with splenic sequestration |
| D57213 | Sickle-cell/Hb-C disease with cerebral vascular involvement |
| D57214 | Sickle-cell/Hb-C disease with dactylitis |
| D57218 | Sickle-cell/Hb-C disease with crisis with other specified complication |
| D57219 | Sickle-cell/Hb-C disease with crisis, unspecified |
| D573 | Sickle-cell trait |
| D574 | Sickle-cell thalassemia |
| D5740 | Sickle-cell thalassemia without crisis |
| D5741 | Sickle-cell thalassemia, unspecified, with crisis |
| D57411 | Sickle-cell thalassemia, unspecified, with acute chest syndrome |
| D57412 | Sickle-cell thalassemia, unspecified, with splenic sequestration |
| D57413 | Sickle-cell thalassemia, unspecified, with cerebral vascular involvement |
| D57414 | Sickle-cell thalassemia, unspecified, with dactylitis |
| D57418 | Sickle-cell thalassemia, unspecified, with crisis with other specified complication |
| D57419 | Sickle-cell thalassemia, unspecified, with crisis |