| G0400 | Acute disseminated encephalitis and encephalomyelitis, unspecified |
| G0401 | Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM) |
| G0402 | Postimmun ac dissem encphlts, myelitis and encephalomyelitis Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis |
| G041 | Tropical spastic paraplegia |
| G042 | Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified |
| G043 | Acute necrotizing hemorrhagic encephalopathy |
| G0430 | Acute necrotizing hemorrhagic encephalopathy, unspecified |
| G0431 | Postinfectious acute necrotizing hemorrhagic encephalopathy |
| G0432 | Postimmunization acute necrotizing hemorrhagic encephalopathy |
| G0439 | Other acute necrotizing hemorrhagic encephalopathy |
| G048 | Other encephalitis, myelitis and encephalomyelitis |
| G0481 | Other encephalitis and encephalomyelitis |
| G0482 | Acute flaccid myelitis |
| G0489 | Other myelitis |
| G049 | Encephalitis, myelitis and encephalomyelitis, unspecified |
| G0490 | Encephalitis and encephalomyelitis, unspecified |
| G0491 | Myelitis, unspecified |
| G05 | Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere |
| G053 | Encephalitis and encephalomyelitis in diseases classd elswhr Encephalitis and encephalomyelitis in diseases classified elsewhere |
| G054 | Myelitis in diseases classified elsewhere |
| G06 | Intracranial and intraspinal abscess and granuloma |
| G060 | Intracranial abscess and granuloma |
| G061 | Intraspinal abscess and granuloma |
| G062 | Extradural and subdural abscess, unspecified |
| G07 | Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere |
| G08 | Intracranial and intraspinal phlebitis and thrombophlebitis |
| G09 | Sequelae of inflammatory diseases of central nervous system |
| G10 | Huntington's disease |
| G11 | Hereditary ataxia |
| G110 | Congenital nonprogressive ataxia |
| G111 | Early-onset cerebellar ataxia |
| G1110 | Early-onset cerebellar ataxia, unspecified |
| G1111 | Friedreich ataxia |
| G1119 | Other early-onset cerebellar ataxia |
| G112 | Late-onset cerebellar ataxia |
| G113 | Cerebellar ataxia with defective DNA repair |
| G114 | Hereditary spastic paraplegia |
| G115 | Hypomyelination - hypogonadotropic hypogonadism - hypodontia Hypomyelination - hypogonadotropic hypogonadism - hypodontia |
| G116 | Leukodystrophy with vanishing white matter disease |
| G118 | Other hereditary ataxias |
| G119 | Hereditary ataxia, unspecified |
| G12 | Spinal muscular atrophy and related syndromes |
| G120 | Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] |
| G121 | Other inherited spinal muscular atrophy |
| G122 | Motor neuron disease |
| G1220 | Motor neuron disease, unspecified |
| G1221 | Amyotrophic lateral sclerosis |
| G1222 | Progressive bulbar palsy |
| G1223 | Primary lateral sclerosis |
| G1224 | Familial motor neuron disease |