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ICD-10-CM Q00 to Q99

Congenital malformations, deformations and chromosomal abnormalities: one chapter of ICD-10-CM.

1,055 codes · page 19 of 22 · every chapter

Congenital non-neoplastic nevus Q82.5 Congenital sacral dimple Q82.6 Other specified congenital malformations of skin Q82.8 Congenital malformation of skin, unspecified Q82.9 Congenital malformations of breast Q83 Congenital absence of breast with absent nipple Q83.0 Accessory breast Q83.1 Absent nipple Q83.2 Accessory nipple Q83.3 Other congenital malformations of breast Q83.8 Congenital malformation of breast, unspecified Q83.9 Other congenital malformations of integument Q84 Congenital alopecia Q84.0 Congenital morphological disturbances of hair, not elsewhere classified Q84.1 Other congenital malformations of hair Q84.2 Anonychia Q84.3 Congenital leukonychia Q84.4 Enlarged and hypertrophic nails Q84.5 Other congenital malformations of nails Q84.6 Other specified congenital malformations of integument Q84.8 Congenital malformation of integument, unspecified Q84.9 Phakomatoses, not elsewhere classified Q85 Neurofibromatosis (nonmalignant) Q85.0 Neurofibromatosis, unspecified Q85.00 Neurofibromatosis, type 1 Q85.01 Neurofibromatosis, type 2 Q85.02 Schwannomatosis Q85.03 Other neurofibromatosis Q85.09 Tuberous sclerosis Q85.1 Other phakomatoses, not elsewhere classified Q85.8 PTEN hamartoma tumor syndrome Q85.81 Other Cowden syndrome Q85.82 Von Hippel-Lindau syndrome Q85.83 Other phakomatoses, not elsewhere classified Q85.89 Phakomatosis, unspecified Q85.9 Congenital malformation syndromes due to known exogenous causes, not elsewhere classified Q86 Fetal alcohol syndrome (dysmorphic) Q86.0 Fetal hydantoin syndrome Q86.1 Dysmorphism due to warfarin Q86.2 Other congenital malformation syndromes due to known exogenous causes Q86.8 Other specified congenital malformation syndromes affecting multiple systems Q87 Congenital malformation syndromes predominantly affecting facial appearance Q87.0 Congenital malformation syndromes predominantly associated with short stature Q87.1 Prader-Willi syndrome Q87.11 Other congenital malformation syndromes predominantly associated with short stature Q87.19 Congenital malformation syndromes predominantly involving limbs Q87.2 Congenital malformation syndromes involving early overgrowth Congenital malformation syndromes involving early overgrowth Q87.3 Marfan syndrome Q87.4 Marfan syndrome, unspecified Q87.40 Marfan syndrome with cardiovascular manifestations Q87.41