ICD-10-CM E00 to E89
Endocrine, nutritional and metabolic diseases: one chapter of ICD-10-CM.
1,242 codes · page 22 of 25 · every chapter
Niemann-Pick disease type D E75.243 Niemann-Pick disease type A/B E75.244 Other Niemann-Pick disease E75.248 Niemann-Pick disease, unspecified E75.249 Metachromatic leukodystrophy E75.25 Sulfatase deficiency E75.26 Pelizaeus-Merzbacher disease E75.27 Canavan disease E75.28 Other sphingolipidosis E75.29 Sphingolipidosis, unspecified E75.3 Neuronal ceroid lipofuscinosis E75.4 Other lipid storage disorders E75.5 Lipid storage disorder, unspecified E75.6 Disorders of glycosaminoglycan metabolism E76 Mucopolysaccharidosis, type I E76.0 Hurler's syndrome E76.01 Hurler-Scheie syndrome E76.02 Scheie's syndrome E76.03 Mucopolysaccharidosis, type II E76.1 Other mucopolysaccharidoses E76.2 Morquio mucopolysaccharidoses E76.21 Morquio A mucopolysaccharidoses E76.210 Morquio B mucopolysaccharidoses E76.211 Morquio mucopolysaccharidoses, unspecified E76.219 Sanfilippo mucopolysaccharidoses E76.22 Other mucopolysaccharidoses E76.29 Mucopolysaccharidosis, unspecified E76.3 Other disorders of glucosaminoglycan metabolism E76.8 Glucosaminoglycan metabolism disorder, unspecified E76.9 Disorders of glycoprotein metabolism E77 Defects in post-translational modification of lysosomal enzymes E77.0 Defects in glycoprotein degradation E77.1 Other disorders of glycoprotein metabolism E77.8 Disorder of glycoprotein metabolism, unspecified E77.9 Disorders of lipoprotein metabolism and other lipidemias E78 Pure hypercholesterolemia E78.0 Pure hypercholesterolemia, unspecified E78.00 Familial hypercholesterolemia E78.01 Pure hyperglyceridemia E78.1 Mixed hyperlipidemia E78.2 Hyperchylomicronemia E78.3 Other hyperlipidemia E78.4 Elevated Lipoprotein(a) E78.41 Other hyperlipidemia E78.49 Hyperlipidemia, unspecified E78.5 Lipoprotein deficiency E78.6 Disorders of bile acid and cholesterol metabolism E78.7 Disorder of bile acid and cholesterol metabolism, unspecified E78.70 Barth syndrome E78.71 Smith-Lemli-Opitz syndrome E78.72