ICD-10-CM E00 to E89
Endocrine, nutritional and metabolic diseases: one chapter of ICD-10-CM.
1,242 codes · page 19 of 25 · every chapter
Chediak-Higashi syndrome E70.330 Hermansky-Pudlak syndrome E70.331 Other albinism with hematologic abnormality E70.338 Albinism with hematologic abnormality, unspecified E70.339 Other specified albinism E70.39 Disorders of histidine metabolism E70.4 Disorders of histidine metabolism, unspecified E70.40 Histidinemia E70.41 Other disorders of histidine metabolism E70.49 Disorders of tryptophan metabolism E70.5 Other disorders of aromatic amino-acid metabolism E70.8 Aromatic L-amino acid decarboxylase deficiency E70.81 Other disorders of aromatic amino-acid metabolism E70.89 Disorder of aromatic amino-acid metabolism, unspecified E70.9 Disord of branched-chain amino-acid metab & fatty-acid metab Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism E71 Maple-syrup-urine disease E71.0 Other disorders of branched-chain amino-acid metabolism E71.1 Branched-chain organic acidurias E71.11 Isovaleric acidemia E71.110 3-methylglutaconic aciduria E71.111 Other branched-chain organic acidurias E71.118 Disorders of propionate metabolism E71.12 Methylmalonic acidemia E71.120 Propionic acidemia E71.121 Other disorders of propionate metabolism E71.128 Other disorders of branched-chain amino-acid metabolism E71.19 Disorder of branched-chain amino-acid metabolism, unspecified E71.2 Disorders of fatty-acid metabolism E71.3 Disorder of fatty-acid metabolism, unspecified E71.30 Disorders of fatty-acid oxidation E71.31 Long chain/very long chain acyl CoA dehydrogenase deficiency Long chain/very long chain acyl CoA dehydrogenase deficiency E71.310 Medium chain acyl CoA dehydrogenase deficiency E71.311 Short chain acyl CoA dehydrogenase deficiency E71.312 Glutaric aciduria type II E71.313 Muscle carnitine palmitoyltransferase deficiency E71.314 Other disorders of fatty-acid oxidation E71.318 Disorders of ketone metabolism E71.32 Other disorders of fatty-acid metabolism E71.39 Disorders of carnitine metabolism E71.4 Disorder of carnitine metabolism, unspecified E71.40 Primary carnitine deficiency E71.41 Carnitine deficiency due to inborn errors of metabolism E71.42 Iatrogenic carnitine deficiency E71.43 Other secondary carnitine deficiency E71.44 Ruvalcaba-Myhre-Smith syndrome E71.440 Other secondary carnitine deficiency E71.448 Peroxisomal disorders E71.5 Peroxisomal disorder, unspecified E71.50 Disorders of peroxisome biogenesis E71.51 Zellweger syndrome E71.510